Download - Penfigoide de las membranas mucosas
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7/23/2019 Penfigoide de las membranas mucosas
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16 dbw
Ykgi|dw fi `ygbwd
b|dk x bgykd|
D`pbkkdw vimwdw phik
Wimwdghm fi d|fb|
Fi|`dvbkbad H_W
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Ni`ba|d`d3 dmi`hd+ kiygbpimhd
_i|ehk nipvhgb3 mb|`dk
_i|ehk khpfhgb3 mb|`dk
_i|ehk |imdk3 mb|`dk
Kd|hmabwgbphd3 ehl|bwhw fi gyi|fdw ubgdkiw
Gbkbmbwgbpd3 mb eyi pbwhlki pb| iwvimbwhw dmdk
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_imehabhfi fi `i`l|dmdw `ygbwdw
HaA x G7
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D- _imehab uykad|
L- _imehab pd|dmibpkwhgb
G- _imehabhfi fi kdw `i`l|dmdw `ygbwdwF- _imehabhfi fi kdw `i`l|dmdw ygbwdw pd|dmibpkwhg
I- Imei|`ifdf Ha D khmidk fik dfykvb
E- Whmf|b`i fi Ligniv
A- whmf|b`i fi \ihvi|
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Ha A** x G7**
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Fiw|fimiw d`pbkkd|iw
wyliphvikhdkiw hm`ymb`ifhdfbw
.h``ymi- `ifhdvif wylipvnhvikhdklkhwvi|hma fhwidwiw( H@WILF
pimehabfi d`pbkkd|
_imehabhfi fi kdw `i`l|dmdw `ygbwdw
fi|`dvbwhw HaD khmidk
fi|`dvbwhw d`pbkkd| g|mhgd fi kd hmedmghd
fi|`dvhvhw ni|pivheb|`i
iphfi|`khwhw d`pbkkd| dftyh|hfd
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Nhwvb|hd
4186 Qhgn`dmm3 pmehab lygdk x bgykd| 4>91 Gbbpi|3 ~i|bwhw gbmcymvhudk
4>18 Udm A|diei3 iwv|ignd`himvb iwimghdk gbmcymvhudk
4>>> @b||hw x \bli|vw3 pmehab fi `ygbwdw gbmvimfimghd whmityhdmvi x fi e|dgdwb vi|dpyvhgb
4>85 Vnbwv 3 pmehab g|mhgb fi kdw `i`l|dmdw
`ygbwdw
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Nhwvb|hd
4844 Vnbwv3 gd|dgvi|wvhgdw `w h`pb|vdmviw
4868 Ghudvvi3 fhei|imghdw nhwvbkahgdw imv|i pmehab x
pimehabhfi
4894 Qdkvi| Kiui|3 pimehabhfi limhamb fi kdw `ygbwdw
4891 L|ymwvhma x _i||x3 1 dmghdmbw gbm d`pbkkdwwyliphf|`hgdw |igy||imviw x ghgdv|hsdkiw wbl|i pkdgdw
fi fhwv|hlyghm ni|pivheb|`i+ im gdlisd x gyikkb+
whm gb`p|b`hwb `ygbwb+ `dxb|d ud|bmiw3
pimehabhfi ghgdv|hsdk .`ygbwb(
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Nhwvb|hd
4887 Cbkx3 pimehabhfi ghgdv|hsdk b `ygbwb3 p|bldlkieb|`d kbgdkhsdfd fi iphfi|`khwhw d`pbkkd| dftyh|hfd
4891 Cdlkbmwjd3 pimehabhfi fi kdw `ygbwdw
489> Kbvd|v x Cdgbl3 kbgdkhsdghm gyvmid mb |d|d+limhamhfdf |ikdvhud .giayi|d x whmityhdw(
fi|`dvhvhw d`pbkkd| `ygbwhmityhdmvi dv|behdmvi
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Nhwvb|hd
4888 Gnhgdab- Hkkhmbhw- YWD+ Gndma+ Dmndkv
_|h`i| Gbmwimwb Hmvi|mdghbmdk fi _imehabhfi fi kdw
@i`l|dmdw @ygbwdw
fiehmi kd vbpba|ded fb`hmdmvi
gb`p|b`hwb wbl|i gydktyhi| `i`l|dmd `ygbwd
gkmhgd+ `vbfb fhdamwvhgb+ g|hvi|hbw vi|dpyvhgbw
Wyp|h`hfb v|`hmb pimehabhfi ghgdv|hsdk pb|tyi ndx
pdghimviw tyi mb fiwd||bkkdm ghgdv|hgiw+ gb`b im dkaymbgdwbw fi deigghm lygdk whm wigyikdw
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Nhwvb|hd
Hmdp|bphdfb ik gdkhehgdvhub fi limhamb3 giayi|d+iwvimbwhw kd|maid x iwbeahgd+
_mehabhfi ghgdv|hsdk fi L|ymwvhma- _i||x3 iw i~gkyhfb: mb
p|iwimvd kiwhbmiw b|dkiw Wyw wigyikdw x ghgdv|hgiw+ wbkb
deigvdm phik gdlikkyfd x gyikkb
Ahmahuhvhw fiwgd`dvhud3 fiwg|hvd im 4>86
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_imehabhfi fi kdw `ygbwdw
a|ypb nivi|bamib fi imei|`ifdfiw d`pbkkd|iwwyliphvikhdkiw+ hmekd`dvb|hdw+ dyvbhm`ymiw+|iwbkyvhudw+ ghgdv|sdkiw x g|mhgdw
deigvdm ymd `ygbwd .kbgdkhsdfb(
ud|hdw ygbwdw .aimi|dkhsdfb(
`ygbwdw lygdk+ bgykd|+ mdwdk+ ed|maid+ kd|maid+iwbeahgd x dmbaimhvdk
im dkaymbw gdwbw+ whm pd|vhghpdghm fi phik
gbm gb`p|b`hwb gyvmib im ym 7?) fi ikkbw
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_imehabhfi fi kdw `ygbwdw
fipwhvbw khmidkiw fi dyvbdmvhgyi|pbw HaA+ HaD+ b fi
d`lbw i Ha@ x G7 im `i`l|dmd ldwdk3 im kd ymhm
iphvikhb- wyliphvikhb
pimehabhfi ghgdv|hsdk+ pimehabhfi limhamb fi kdw
`ygbwdw+ pimehabhfi b|dk+ ahmahuhvhw fiwgd`dvhud+
pimehabhfi ghgdv|hsdk bgykd| b fi|`dvhvhw d`pbkkd|
`ygbwhmityhdmvi x dv|behdmvi fi Kbvd|v x Cdgbl
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_imehabhfi fi kdw `ygbwdw
Imei|`ifdf uiwhgbd`pbkkd| |d|d+ g|mhgd+ gbm
p|ifhkigghm pb|`i`l|dmdw `ygbwdw3 b|dk xbgykd|Vimfimghd d ficd| ghgdv|hgiw
9-5 fgdfd
L_4>? .G-vi|`hmdk(Iphkha|hmd3 4?)Kd`hmhmd 9
Dg gbmv|d 73 im vbfbw kbw pdghimviw Dg gbmv|d 73 pbgbw Dg gbmv|d 73 `yx pbgbw
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SBMD FI KD YMHM FI\@B-I_HF\@HGD
Tyi|dvhmbghvb ldwdk Tyi|dvhmbghvb ldwdk
Fiw`bwb`d
Ni`hfiw`bwb`d Ni`hfiw`bwb`d
K`hmd kghfd
K`hmd fimwd
gbkaimb vhpb HU
Ehl|hkkdw fi dmgkdci. gbkaimb vhpb UHH(
_kdgd fi dmgkdci
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Ehkd`imvbw hmvi|`ifhbw_kigvhmd
_kdgd hmvi|mdL_
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Dmvaimbw lkdmgb hfimvhehgdfbw im _@Gbmbghfbw3
Dmvaimb fik pimehabhfi d`pbkkd| 4 .L_?+ Gbkaimb vhpb ^UHH(
Kd`hmhmd 9 .gdfimdw 77 x Jf
_|bvimd iphvikhdk fi 4
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Dmvaimbw lkdmgb x wyw hmvi|dgghbmiw
`bkigykd|iw . 4 (
L_ 4>?3 hmvia|hmd 56
L_?
gbkaimb UHH
Kd`hmhmd 53 kd`hmhmd 9
lk h h
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Dmvaimbw lkdmgb x wyw hmvi|dgghbmiw
`bkigykd|iw .? .MG 45D(
kd`hmhmd 9
Hmvia|hmd 63 hmvia|hmd 5
L_4>?
pkigvhmd
kd`hmhmd 9
Gbkaimb UHH3 kd`hmhmd 9
gbkaimb vhpb HU
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Wyla|ypbw pb| hm`ymbnhwvbty`hgd
4- Dmvhiphkha|hmd .kd`hmhmd 9(
Kbw Dg HaA wi ymim dk kdfb f|`hgb fy|dmvi ik wpkhv
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Gd|dgvi|wvhgdw
@yci|iw- 9? d 1? dbw
Lbgd3 >? d 4?? )- Imgd3 5? )
Bcbw3 9? d 5?)
_hik .gdlisd x gyikkb(3
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kiwhbmp|h`d|hd3d`pbkkd
|ypvy|d
i|bwhmb ykgi|d
gy|dghm
ghgdv|hs
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`ygbwd b|dk .>9)(
gbmcymvhud .56)(
phik .)(
dmb .6)(
iwedab .6)(
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Ehay|i 45 Limham `ygbyw `i`l|dmi pi`pnhabhf
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Ehay|i 45 Limham `ygbyw `i`l|dmi pi`pnhabhf
Kyifvji _ iv dk \dfhba|dpnhgw
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imgd .56)(
`ygbwd xyadk .9>)(
pdkdfd| .
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i|hvi`d x ifi`d ahmahudk kiuiw ndwvd eb|`dghm fi
d`pbkkdw+ i|bwhbmiw x kgi|dw
`dw e|igyimvi3 ahmahuhvhw fiwgd`dvhud b i|bwhud
@buhkhfdf fimvdk3 @DK _\BMBWVHGB
|ipd|dghm `yx kimvd+ vimfimghd d eb|`dghm fi
ghgdv|hgiw+ ehl|bwhw x whmityhdw
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Ahmavhuhvhw fiwgd`dvhud
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Ahmavhuhvhw fiwgd`dvhud_|hms 487
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gbmcymvhuhvhw g|mhgd3 tyi`dsm+h||hvdghm+ kda|h`ib xeb|`dghm fi `ygbwhfdf
dkvi|mdmghd im i~dgi|ldghm x |i`hwhm
p|ba|iwhm d ehl|bwhw gbmcymvhudk wyliphvikhdk
wh`lked|bm .dfni|imghdw(+ |ifygghm fik e|mh~ hmei|hb|
p|pdfb wi dfnhi|i d akblb bgykd| x kb ehcd
blkhvi|dghm fi wdgb gbmcymvhudk3 dmtyhkblked|bm
v|htyhdwhw .b|himvdghm dmb|`dk fi kdw piwvddw(
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imv|bphm
hmekd`dghm x ehl|bwhw kkiudm d fiwv|ygghm
fi gbmfygvbw x akmfykdw kda|h`dkiw+ gbm ~i|bwhw+
x kgi|dw gb|midmdw pb| v|dy`dw pityibw akblb bgykd| i~pyiwvb pb| h`pbwhlhkhfdf fi `buhkhsd| kbw
p|pdfbw
bpdghfdfiw gb|midmdw pb| gb|mhehgdghm fik iphvikhbwypi|ehghdk eb|`dghm fi vichfb fi a|dmykdghm .pdmmywgb|midmb( gbm giayi|d im
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Wyla|ypbw gkmhgbw
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Wyla|ypbw gkmhgbw
4 _imehabhfi `ygbwb gbm Dg dmvh-kd`hmhmd-9 .dmvh-iphkha|hmd(3
d`pbkkdw x ghgdv|hgiw im `ygbwdw b|dk x bgykd|+ d uigiw iw pd|dmibpkwhgb
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_HIK WI_D\DFD GBM GkMd 4 @bkd|
Gkykd ldwdk
.L_Da4+ L_Da
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Bevdk`kbab
B\K
Fi|`dvkbab
Y|kbab
Adwv|bimvi|kbab
_|bgvkbab
Iwvb`dvkbab
V v h v f k _@@
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V|dvd`himvb fik _@@
Im ldwi d kbw whvhbw fi gb`p|b`hwb dmdv`hgb
_dghimviw fi ldcb |hiwab3 gbm wbkb deigvdghm fi
`ygbwd b|dk b gbm kiwhbmiw b|dkiw x im phik
_dghimviw fi dkvb |hiwab3 pd|vhghpdghm fi `ygbwd
bgykd|+ aimhvdk+ mdwbed|maid+ iwbeahgd+ dmdk x"bkd|maid
Gndm KW+ Dn`if D\+ Dmndkv AC+ iv dk _|h`i| gbmwimwb hmvi|mdghbmdk wbl|i pimehabhfi
fi kdw `ygbwdw3 g|hvi|hbw fi fiehmhghm+ fhdamwvhgb+ edgvb|iw pdvaimbw+ v|dvd`himvb
`fhgb i hmfhgdfb|iw fi p|bmwvhgb D|gn Fi|`dvbk
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fi ldcb |hiwabImei|`ifdf b|dk kh`hvdfd whm p|ba|iwhm |phfd3
Vi|dphd vphgd gb`b gbdfxyudmvi b `bmbvi|dphd3 iwvi|bhfiw vphgbw
ghgkbwpb|hmd
vdg|bkh`ywIhwim F+ Ikkhw GM+ Ubb|niiw CC Vbphgdk gxgkbwpb|hmi eb| b|dk lykkbyw fhwb|fi|w C D`Dgdf Fi|`dvbk 488?:
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Dmviw Fiwpyw
V|dvd`himvb fi _@@
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fi ldcb |hiwabImei|`ifdf kiui whm p|ba|iwhm |phfd + gbm `mh`d
b mykd |iwpyiwvd d vi|dphd vphgd3
Fdpwbmd3 hmhghd| gbm
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Dmviw Fiwpyw
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Dmviw Fiwpyw
V|dvd`himvb fi _@@
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fi dkvb |hiwab
Mykd |iwpyiwvd d FFW+ imei|`ifdf wiui|d b gbm |phfd
_|ba|iwhm d bv|dw `ygbwdw3
_|ifmhwbmd3 4 d 49 `a"ja"fd+ ud|hbw `iwiw
Wypki`imvbw fi gdkghb+ uhvd`hmd F cymvb gbm
lhebwebmdvbw
D kd |i`hwhm gkmhgd+ |ifygh| a|dfydk`imvi fbwhw
@dmvimh`himvb3 fbw dbw dp|b~h`dfd`imvi
V|dvd`himvb fi _@@
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fi dkvb |hiwab
Edkvd fi `d|gdfd `icb|d im 7 `iwiw fi gb|vhgbhfiw bdeigghm d whvhb fi dkvb |hiwab+ .wypi|ehghi bgykd|(3
Dsdvhbp|hmd+ `ivbv|i~dvb b ghgkbebwed`hfd ub
\iuhwd| fehghv akygbwd-5-ebwedvb+Iudkyd| |hiwab fi ni`khwhw pb| dmi`hd ni`bkvhgd+
`ivdni`bakblhmi`hd y bv|bw ieigvbw wigymfd|hbw
hfhbwhmg|vhgbw gb`b da|dmykbghvbwhw+ nipdvhvhw b wmf|b`i
fi nhpi|wimwhlhkhfdf d FFW
V|dvd`himvb fi _@@
f k h
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fi dkvb |hiwab
Imei|`ifdf wiui|d+ b gbm |phfd p|ba|iwhm3
Ghgkbebwed`hfd3 hmhghd| cymvb gbm iwvi|bhfiw whwv`hgbw
4 d
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fi dkvb |hiwab Dsdvhbp|hmd3 dmkbab fi py|hmd dgvhub tyi wi hmgb|pb|d d
DFM x D\M gbm gbmwhayhimvi hmnhlhghm fik `ivdlbkhw`b py|hmdw x fhuhwhm gikykd|
Fbwhw3 4 d 6 `a " ja " fd+ fipimfhimfb fik mhuik fi
vhbpy|hmd `ivhkv|dmwei|dwd Ieigvbw dfui|wbw a|duiw3 kiygbpimhd+ pdmghvbpimhd+
hmeigghbmiw+ vy`b|iw `dkhambw x wmf|b`i fi
nhpi|wimwhlhkhfdf
Wiayh`himvb3 ni`ba|d`d gb`pkivb x eymghm nipvhgd
V|dvd`himvb fi _@@
f kv h
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fi dkvb |hiwab @ivbv|i~dvb3 Wbkhvd|hb im vi|dphd fi @@_ bgykd|
Fbwhw3 9 d 8) fi pdghimviw gbm @@
x 4??) gbm @@_ d f|badw
Ieigvbw dfui|wbw a|duiw3 nipdvbvb~hghfdf .ehl|bwhw nipvhggh||bwhw(+ miy`bmhvhw dayfd hfhbwhmg|whgd+ ehl|bwhw pyk`bmd
pdmghvbpimhd+ x vy`b|iw `dkhambw
Gbmv|bk3 ni`ba|d`d gb`pkivb+ p|yildw |imdkiw+ fi eymgh
nipvhgd Lhbpwhd nipvhgd fiwpyw fi ymd fbwhw dgy`ykdvhufi 4+9 d 7 a|d`bw
V|dvd`himvb fi _@@
f kv h
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fi dkvb |hiwab @hgbeimbkdvb `beivhkb3 hmnhli fiwnhf|baimdwd hmbwhmd
`bmbebwedvb+ gbm lkbtyib fi wmviwhw fi mbub fi py|hmdwV|dfyghfb gb`b hmnhlhghm fi |iwpyiwvd p|bkhei|dvhud fi
gkykdw L x V
Fbwhw3 4??? d
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fi dkvb |hiwab HA HU3 lkbtyid |igipvb|iw Eg+ dkvi|d p|bfygghm x dmvdabmhw`b
ghvbtyhmdw+ hmnhli gb`pki`imvb x miyv|dkhsd dyvbdmvhgyi|pbwgh|gykdmviw
Fbwhw3 < d 7 a"ja" 7 d 9 fdw"7 d 6 wi`dmdw
\idgghm d kd hmeywhm3 i|hvi`d+ giedkid+ iwgdkbe|bw+ mywidw+
vdtyhgd|fhd+ nhpbvimwhm x whlhkdmghdw Yvhkiw dmvhnhwvd`mhgbw+pd|dgivd`bk b iwvi|bhfiw pb| ud hmv|duimbwd
Bv|bw ieigvbw dfui|wbw3 dmdehkd~hw+ gbdaykdghm hmv|dudwgykd|
fhwi`hmdfd+ v|b`lbwhw i hmwyehghimghd |imdk dayfd
Ni`ba|d`d gb`pkivb+ p|yildw |imdkiw+ eymghm nipvhgd+ pdmi
fi nipdvhvhw+ UHN+ HaD+ E\ x g|hbakblykhmdw
Bv|dw vi|dphdw fi _@@
fi dkvb |hiwab
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fi dkvb |hiwab
Daimviw dmvhedgvb| fi mig|bwhw vy`b|dk 3
Ivdmi|gipv i Hmekh~h`dl Fdgkhsy`dl+ dmvdabmhwvd fik |igipvb| fi hmvi|kiyghmd-< 3
`bmbvi|dphd fik _@@ bgykd|
\hvy~h`dl3 dmvh-GF
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imei|`ifdf bgykd|
Gb`pki`imvd|hd d vi|dphd whwv`hgd
Gb|vhgbwvi|bhfiw vphgbw x wylgbmcymvhudkiw3pdkhd| wmvb`dw
Mb iehgdgiw pd|d fivimi| p|ba|iwhm fi kd imei|`ifdf
Hmnhlhfb|iw fi kd gdkghmiy|hmd+ ghgkbwpb|hmd D x
vdg|bkh`yw3 |iwykvdfbw ud|hdlkiw
@hvb`hghmd G3 dktyhkdmvi tyi hmnhli wmviwhw fi DFM x
p|bkhei|dghm fi ehl|blkdwvbw3 fiwpyw fi khwhw tyh||ahgd
fi whmityhdw gbmcymvhudkiwFbmmimeikf IF+ _i||x NF+ Qdkki|wvihm D+ iv dk Wylgbmcymgvhudk `hvb`xghm G eb| vni v|idv`imv be
bgykd| ghgdv|hghdk pi`pnhabhf Bpnvndk`bkbax 4888: 4?5 31fhwgywwhbm 18
Vi|dphd vphgd fi
imei|`ifdf bgykd|
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imei|`ifdf bgykd|
Lkied|hvhw dmvi|hb| x pbwvi|hb|+ x v|htyhdwhw3 gb`p|iwdw
gdkhimviw fbw uigiw dk fd
Kdudfb fi p|pdfbw gbm gnd`p fi lil fhkyhfb
dpkhgdghm mbgvy|md fi pb`dfd gbm dmvhlhvhgbw gb`b
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7/23/2019 Penfigoide de las membranas mucosas
65/71
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7/23/2019 Penfigoide de las membranas mucosas
66/71
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7/23/2019 Penfigoide de las membranas mucosas
67/71
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7/23/2019 Penfigoide de las membranas mucosas
68/71
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7/23/2019 Penfigoide de las membranas mucosas
69/71
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7/23/2019 Penfigoide de las membranas mucosas
70/71
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7/23/2019 Penfigoide de las membranas mucosas
71/71