casos patológicos del servicio de fisiología pulmonar de niÑos
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CASOS PATOLOGICOS DEL SERVICIO DE
FISIOLOGIA PULMONAR
PEDIATRICOS
Fibrosis quística
Fibrosis quística
Fibrosis quística
Fibrosis quística
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 1.29 0.70 54 0.70 54
FEV 1.09 0.30 27 0.30 27
REL 85 43 -42 43 -42
FMAX 2.3 0.90 38 0.90 38
F 25-75 1.6 0.20 13 0.20 13
F75-85 0.64 0.07 11 0.07 11
HbO2 78S=2, E=7, P=16, T=1.07, IMC:14
Fibrosis quísticaPatrón mixto de grado moderado a muy severo
Fibrosis quística
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 2.18 1.25 57 1.53 70
FEV 1.86 0.61 33 0.77 41
REL 85 49 -36 50 -35
FMAX 4.00 1.80 45 2.10 53
F 25-75 2.60 0.20 7 0.30 11
F75-85 1.09 0.06 5 0.10 9
HbO2 83S=1, E=12, P=25, T=1.34, IMC:13.9
Fibrosis quística
Fibrosis quística
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 2.41 0.71 32 0.71 32
FEV 2.05 0.44 21 0.44 21
REL 85 57 -28 57 -28
FMAX 44 2.30 52 2.30 52
F 25-75 2.90 0.20 7 0.20 7
F75-85 1.20 0.08 7 0.08 7
HbO2 70
Fibrosis quística
S=2, E=12, P=25.5, T=1.39, IMC:13.2
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 3.42 1.84 54 1.84 54
FEV 2.91 0.88 30 0.88 30
REL 85 48 -37 48 -37
FMAX 6.20 2.70 43 2.70 43
F 25-75 4.10 0.30 7 0.30 7
F75-85 1.71 0.10 6 0.10 6
HbO2 81
Fibrosis quística
S=2, E=15, P=43.8, T=1.57, IMC:17.8
Fibrosis quística
PRED BASAL % POS BR %
FVC 1.73 1.21 70 1.21 70
FEV 1.47 0.69 46 0.69 46
REL 85 55 -30 55 -30
FMAX 3.1 2.00 64 2.00 64
F 25-75 2.1 0.40 19 0.40 19
F75-85 0.86 0.17 19 0.17 19
HbO2 93
Fibrosis quística
S=1, E=9, P=19, T=1.22, IMC:
Sd. Polland
Sd. Polland
DextrocardiaAsimetría toracicaHipoplasia pulmonar izq
PRED BASAL % POSBR %
FVC 1.50 1.35 90 1.35 90
FEV 1.28 1.15 90 1.15 90
REL 85 85 0 85 0
FMAX 2.74 3.05 128 3.05 128
F 25-75 1.82 2.00 110 2.00 110
F75-85 0.75 0.80 106 0.80 106
HbO2 94
Sd. Polland
S=2, E=5, P=21.8, T=1.15, IMC:16.44
Bronquiectasias
Bronquiectasias
Bronquiectasias
Bronquiectasias
PRED BASAL % POSBR %
FVC 2.33 1.38 59 1.69 72
FEV 1.95 0.70 36 0.82 42
REL 58 51 -40 48 -42
FMAX 4.38 1.50 34 1.50 34
F 25-75 2.67 0.30 11 0.30 11
F75-85 0.87 0.10 11 0.10 11
HbO2 94
Bronquiectasias
S=2, E=11, P=25, T=1.32, IMC:14.35
Fibrosis quística
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 2.10 0.83 39 0.90 43
FEV 1.75 0.47 27 0.53 30
REL 87 57 -33 59 -31
FMAX 4.00 2.30 57 3.00 75
F 25-75 2.47 0.20 8 0.20 8
F75-85 0.79 0.06 8 0.06 8
HbO2 78
Fibrosis quística
S=2, E=10, P=23, T=1.27, IMC:14.26
Neumonía intersticial
Neumopatía intersticial
Neumopatía intersticial
PRED BASAL % POSBR %
FVC 2.95 1.52 51 1.52 51
FEV 2.46 1.40 57 1.40 57
REL 85 92 7 92 7
FMAX 5.36 4.00 75 4.00 75
F 25-75 3.24 2.20 68 2.20 68
F75-85 1.01 0.68 68 0.68 68
HbO2 52
Neumonía intersticial
S=2, E=14, P=22, T=1.43, IMC:10.76
Fibrosis quística
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 1.38 0.80 58 0.80 58
FEV 1.15 0.40 35 0.49 43
REL 86 50 -36 61 -25
FMAX 2.72 2.00 73 2.00 73
F 25-75 1.88 0.80 42 0.80 42
F75-85 0.35 0.15 42 0.15 42
HbO2 86%
Fibrosis quística
S=1, E=8, P=16, T=1.06, IMC:14.24
Neumonía en resolución
Neumonía en resolución
PRED BASAL % POSBR %
FVC 2.19 1.81 82 1.81 82
FEV 1.88 1.57 82 1.57 82
REL 86 87 1 87 1
FMAX 4.22 4.00 95 4.00 95
F 25-75 2.42 2.10 87 2.10 87
F75-85 0.99 0.80 82 0.80 82
HbO2
S=1, E=8, P=38, T=1.30, IMC:22.49
Neumonía en resolución
Pb. Hipoplasia pulmonar
Pb. Hipoplasia pulmonar
PRED BASAL % POS BR %
FVC 4.34 1.71 39 1.71 39
FEV 2.92 1.13 29 1.13 29
REL 89 66 -22 66 -22
FMAX 10.81 3.30 31 3.30 31
F 25-75 4.79 0.80 17 0.80 17
F75-85 1.77 0.20 11 0.20 11
S=1, E=17, P=37, T=1.56, IMC:15.20
Pb. Hipoplasia pulmonar
REPOSO EJERCICIO O2
PaO2 68
PaCO2 30
pH 7.40
HbO2 92
Pb. Hipoplasia pulmonar
Estenosis traqueal
PRED BASAL % POS BR %
FVC 3.42 2.08 61 2.08 61
FEV 2.99 1.82 61 1.82 61
REL 88 87 0 87 0
FMAX 6.20 2.60 42 2.60 42
F 25-75 3.43 2.20 64 2.20 64
F75-85 1.30 1.20 92 1.20 92
S=2, E=13, P=40.7, T=1.51, IMC:17.85
Estenosis traqueal
94 %
Foto
Foto
PRED BASAL % POSBR %
FVC 2.66 0.50 19 0.50 19
FEV 2.31 .035 15 .035 15
REL 88 70 -18 70 -18
FMAX 4.89 1.00 20 1.00 20
F 25-75 3.00 0.30 10 0.30 10
F75-85 0.95 0.10 10 0.10 10
HbO2 70
Fibrosis quística
S=1, E=13, P=25, T=1.38, IMC:13.13
Fibrosis quística
REPOSO EJERCICIO O2
PaO2 35
PaCO2 29
pH 7.43
HbO2 70
Bronquitis crónica
Bronquitis crónica
PRED BASAL % POSBR %
FVC 3.73 3.17 13 3.17 13
FEV 3.26 2.45 11 2.45 11
REL 88 77 -18 77 -18
FMAX 6.67 6.00 15 6.00 15
F 25-75 3.67 2.00 8 2.00 8
F75-85 1.35 0.74 7 0.74 7
HbO2
Bronquitis crónica
S=1, E=14, P=39, T=1.55, IMC:16.23
Bronquitis crónica
REPOSO EJERCICIO O2
PaO2 66 402
PaCO2 27 18
pH 7.42 7.54
HbO2 94 99
CCA % 5.61
Bronquiolitis obliterante
PRED BASAL % POSBR %
FVC 3.29 2.25 68 2.25 68
FEV 2.88 1.16 40 1.16 40
REL 88 52 -36 52 -36
FMAX 5.98 4.30 72 4.30 72
F 25-75 3.36 0.40 12 0.40 12
F75-85 1.24 0.10 8 0.10 8
HbO2 94S=2, E=13, P=45, T=1.49, IMC:20.27
Bronquiolitis obliterante
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 3.66 1.85 51
FEV 3.20 1.21 38
REL 88 65 -23
FMAX 6.55 3.80 58
F 25-75 3.64 0.60 17
F75-85 1.33 0.20 15
HbO2 72S=2, E=14, P=40, T=1.54, IMC:16.87
Fibrosis quística
Fibrosis quística
Fibrosis quística
PRED BASAL % POSBR %
FVC 2.23 1.39 62 1.49 67
FEV 1.93 0.75 39 0.75 39
REL 87 54 -33 50 -36
FMAX 4.22 3.70 88 3.70 88
F 25-75 2.55 0.20 8 0.20 8
F75-85 0.89 0.07 8 0.07 8
HbO2 87
Fibrosis quística
Neumonía intersticial difusa
PRED BASAL % POSBR %
FVC 1.85 0.85 46 0.85 46
FEV 1.60 0.73 46 0.73 46
REL 86 86 0 86 0
FMAX 3.65 2.60 71 2.60 71
F 25-75 2.11 0.80 38 0.80 38
F75-85 0.88 0.30 34 0.30 34
HbO2 90
Neumonía intersticial difusa
S=1, E=6, P=38.5, T=1.22, IMC:25.87
Ca. metastático.
Ca. metastático.
Ca. metastático.
PRED BASAL % POSBR %
FVC 2.46 1.70 69 1.70 69
FEV 2.14 1.43 67 1.43 67
REL 87 84 -3 84 -3
PEF 4.54 5.20 114 5.20 114
F 25-75 2.87 2.10 73 2.10 73
F75-85 0.85 0.62 73 0.62 73
HbO2 94S=1, E=13, P=24.5, T=1.34, IMC: 13.64
Ca. metastático.
Neurofibromatosis múltiple
Neurofibromatosis múltiple
Neurofibromatosis múltiple
PRED BASAL % POSBR %
FVC 2.04 1.68 82 1.68 82
FEV 1.77 1.45 82 1.45 82
REL 87 86 -1 86 -1
PEF 3.78 3.70 98 3.70 98
F 25-75 2.65 2.40 90 2.40 90
F75-85 0.53 0.45 85 0.45 85
HbO2 94S=1, E=14, P=26.5, T=1.24, IMC: 17.23
Neurofibromatosis múltiple
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